Arnold’s chiary malformation is a rare congenital defect which may be defined as a cystic collection of serous fluid in the mouth with abnormal peripheral lymphatic drainage and ipsilateral fat and muscle atrophy. The pathogenesis of Arnold’s chiary malformation is obscure, as the condition has been reported to be associated with congenital heart disease, thyroid dysplasia, and septal defects with or without cardiomyopathies. We report two cases of Arnold’s chiary malformation in patients with myopathy associated with an acquired defect of the posterior longitudinal ligament of the heart and with a small foramen ovale defect. Both patients underwent surgery and had excellent results with no recurrence of Arnold’s chatory malformation. Although the myopathy is not directly related to Arnold’s chiary malformation, we believe that this disorder should be considered in the differential diagnosis when an infant with myopathy has a history of congenital heart disease or acquired cardiomyopathies.
1 Introduction Arnold’s chiary malformation (ACCM) was first described by Royston and Strindberg in 1947 [ 1 ] as a cystic collection of serous fluid within the mouth. The clinical features include an accumulation of serous fluid often associated with a mucocele, anterior facial asymmetry, chronic swelling, ipsilateral
What is Arnold’s Chiary Malformation?
Arnold’s chiary malformation is a congenital birth defect that is characterized by the overgrowth of hair on the lips, commonly called ‘chiary.’ The overgrowth of hair may cause redness, soreness, and difficulty in eating or drinking. Arnold’s chiary malformation is most commonly diagnosed in children between one and four years old. There is no known cure for Arnold’s chiary malformation, but treatment may include surgery to remove the hair and/or medication to reduce the overgrowth of hair.
Epidemiology
Arnold’s Chiary Malformation (ACM), also known as Arnold-Chiari malformation or Chiari I malformation, is a neurological disorder that affects the spine. ACM is a result of abnormal growth of the cerebellum, which can compress the spinal cord. The condition typically progresses slowly and may not be noticed until late in life. There is no cure for ACM, but treatment options include surgery, physical therapy, and drug therapy and may help to prevent neurological damage. Some children with ACM may develop hydrocephalus and have accompanying neurological complications such as loss of vision or hearing, movement disorders, and seizures, which can be treated through surgery.
Arnold’s Chiary Malformation (ACM), also known as Arnold-Chiari malformation or Chiari I malformation, is a neurological disorder that affects the spine. ACM is a result of abnormal growth of the cerebellum, which can compress the spinal cord. The condition typically progresses slowly and may not be noticed until late in life. There is no cure for ACM, but treatment options include surgery, physical therapy, and drug therapy and may help to prevent neurological damage. Some children with
Etiology
Arnold’s Chiary Malformation is a condition that results from the fusion of two normally separate portions of the facial skeleton. The condition, which is also known as Arnold-Chiari malformation or Chiari malformation type I, is most commonly found in children and young adults but can also occur in adults. The malformation typically affects the base of the skull (the cranial base), and can cause difficulty breathing, swallowing, and speaking.
The cause of Arnold’s Chiary Malformation is unknown, but it may be caused by a number of factors including genetics, brain abnormalities, and birth injuries. The condition is most commonly diagnosed during childhood or early adulthood but can occasionally be seen in adults. Symptoms of Arnold’s Chiary Malformation vary depending on the location and severity of the malformation, but often include difficulty breathing, swallowing, speaking, and eating.
There is no cure for Arnold’s Chiary Malformation, but treatments range from surgical procedures to medication. In some cases, surgery may be necessary to correct the malformation and improve symptoms. If surgery is not possible or if treatment doesn’t improve symptoms, patients may require lifelong medical care.
Symptoms
Arnold’s chiary malformation (ACM) is a congenital disorder that affects the mandible. ACM is usually diagnosed in childhood, but can also be found in adults. ACM most commonly affects the lower jaw, but it can also occur on the upper jaw. The most common symptoms of ACM are difficulty chewing and swallowing, as well as facial deformity. There is no known cure for ACM, but treatment typically includes surgical stabilization and rehabilitation.
Who gets Arnold’s Chiary Malformation?
Arnold’s Chiary Malformation is a rare disorder that affects the salivary glands. The malformation can result in dry mouth, toothache, or other mouth problems. Arnold’s Chiary Malformation is most common in children but can also occur in adults. The cause of Arnold’s Chiary Malformation is not known, but it may be linked to genetics or environmental factors. There is no known cure for Arnold’s Chiary Malformation, but treatment may include mouth care, medication, and surgery.
How does Arnold’s Chiary Malformation get managed?
Arnold’s Chiary Malformation is a benign tumor that typically affects the teeth and jawbone. It is named after Arnold von Baer, a German anatomist who first described it in 1827. The tumor grows within the jawbone and can cause deformity, pain, and difficulty eating and speaking. Management of Arnold’s Chiary Malformation typically includes surgery to remove the tumor and reconstruction of the jawbone.
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